The Chapel Hill Consensus Conferences (CHCC) (1994 and 2012) are a pair of international conferences which addressed the need of standardized classification system for systemic vasculitides.Jennette JC; Nomenclature of systemic vasculitides. Proposal of an international consensus conference; Arthritis Rheum 2013Jennette, JC; Overview of the 2012 Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides; Clinical and Experimental Nephrology, 2013

2012 Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides

Classification Group Diseases Large-vessel vasculitis (LVV) Takayasu's arteritis (TAK); Giant-cell arteritis (GCA) Medium-vessel vasculitis (MVV) Polyarteritis nodosa (PAN), Kawasaki disease (KD) Small vessel vasculitis (SVV) ANCA-associated vasculitis (AAV); Immune complex SVV Variable vessel vasculitis (VVV) Behcet's disease (BD); Cogan's syndrome (CS) Single Organ Vasculitis (SOV) Cutaneous leukocytoclastic angiitis; cutaneous arteritis; primary central nervous system vasculitis; isolated aortitis; others Vasculitis associated with systemic disease Lupus vasculitis; Rheumatoid vasculitis; Sarcoid vasculitis; others Vasculitis associated with probable etiology Hepatitis C virus-associated cryoglobulinemic vasculitis; Hepatitis B virus-associated vasculitis; Syphilis-associated aortitis; Drug-associated immune complex vasculitis; Cancer-associated vasculitis; others

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