Glutaryl-CoA

Glutaryl-coenzyme A is an intermediate in the metabolism of lysine and tryptophan.

Clinical Significance Deficiency of glutaryl-CoA dehydrogenase causes glutaric acidemia type 1, an autosomal recessive metabolic disorder.In this disorder, impaired metabolism of glutaryl-CoA is associated with elevated levels of organic acids, including glutaric acid and 3-hydroxyglutaric acid .

See also Glutaryl-CoA dehydrogenase

References