Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase) is a mitochondrial transferase enzyme () involved in the metabolism of palmitoylcarnitine into palmitoyl-CoA. A related transferase is carnitine acyltransferase.

Molecules

Human forms There are four different forms of CPT in humans:

CPT1A – associated with Carnitine palmitoyltransferase I deficiency CPT1B CPT1C CPT2 – associated with carnitine palmitoyltransferase II deficiency

See also

References

External links – Acyltransferases ChoActase / COT / CPT family in PROSITE Choline/Carnitine o-acyltransferase family in Pfam