Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase) is a mitochondrial transferase enzyme () involved in the metabolism of palmitoylcarnitine into palmitoyl-CoA. A related transferase is carnitine acyltransferase.
Molecules
Human forms There are four different forms of CPT in humans:
CPT1A – associated with Carnitine palmitoyltransferase I deficiency CPT1B CPT1C CPT2 – associated with carnitine palmitoyltransferase II deficiency
See also
References
External links – Acyltransferases ChoActase / COT / CPT family in PROSITE Choline/Carnitine o-acyltransferase family in Pfam